Adult Cystic Fibrosis

Cystic fibrosis is an inherited condition that damages the lungs, digestive system and surrounding organs. This condition is caused by a defective gene that directs the production of mucus, sweat and other fluids our bodies need to survive.

Normally, mucus is slippery and thin, protecting our organs and tissues. However people with cystic fibrosis have mucus that is thick and sticky, which can cause blockages, infections and other types of harm.

Cystic fibrosis is typically diagnosed during childhood or the teenage years, and causes lung function to decline over time.

Adults with cystic fibrosis often have lung problems, including:

• Wheezing or shortness of breath
• Chronic cough that produces blood or mucus
• Frequent respiratory infections

At MultiCare, we support adults with cystic fibrosis after they have transitioned out of pediatric care. We also provide care for adults who are newly diagnosed. While there is no cure for this condition, following your treatment plan and taking steps to lower your risk of complications can help you live an active, fulfilling life.

Your primary care provider and your pulmonologist will help you manage the condition through a variety of strategies. Your treatment plan may include:

Airway clearance therapy. The goal of this therapy is to loosen the mucus in your lungs. Your provider may gently push against your chest and back to manually clear your airways. Certain devices such as vibrating vests and breathing machines can also dislodge trapped mucus.

Lifestyle changes. Following specific dietary and physical activity recommendations can help keep you in the healthiest shape possible.

Medications. Your provider may prescribe antibiotics to prevent lung infections, bronchodilators to make it easier to breathe or medications that help clear mucus from your airways.

Nutritional supplements. Cystic fibrosis can make it difficult to absorb nutrients from food. Taking pancreatic enzymes, vitamins and supplements can help you get adequate nutrition.